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EXP000633

Paper

Erythroid-Progenitor-Targeted Gene Therapy Using Bifunctional TFR1 Ligand-Peptides in Human Erythropoietic Protoporphyria (2019)

Peptide

P1-9R

Sequence: TFR1 ligand peptide – Cys-(D-R9)-Cys (exact ligand sequence not disclosed)

RNA

antisense oligonucleotide (AON)

All experiment fields

Experiment Id EXP000633
Paper Erythroid-Progenitor-Targeted Gene Therapy Using Bifunctional TFR1 Ligand-Peptides in Human Erythrop
Peptide P1-9R
Delivery Success Class no
In Vivo Flag no
Uptake Confirmed yes
Label Confidence high
In Vitro Functional Effect yes
Endosomal Escape Evidence yes
Peptide Concentration Charge ratio 5:1 (peptide:AON)
Rna Concentration 428 nM
Mixing Ratio 5:1
Formulation Format CPP–AON nanocomplex
Formulation Components P1-9R + AON-V1
Size Nm 200.00
Zeta Mv
Model Scope in_vitro
Model Type in vitro
Cell Lines Or Primary Cells LBCLs; UT7-EPO; primary CD34+ erythroid progenitors
Animal Model
Administration Route
Output Type splice correction / gene expression rescue
Output Value Normalization of WT FECH mRNA and protein; ↓PPIX
Output Units
Output Notes Efficient TFR1-mediated uptake and sustained splice correction
Toxicity Notes No detectable cytotoxicity
Curation Notes