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EXP001689

Paper

Arginine-rich cell-penetrating peptide dramatically enhances AMO-mediated ATM aberrant splicing correction and enables delivery to brain and cerebellum (2011)

Peptide

(RXRRBR)2XB

Sequence: (RXRRBR)(RXRRBR)XB

RNA

AMO (antisense morpholino oligonucleotide)

All experiment fields

Experiment Id EXP001689
Paper Arginine-rich cell-penetrating peptide dramatically enhances AMO-mediated ATM aberrant splicing corr
Peptide (RXRRBR)2XB
Delivery Success Class no
In Vivo Flag no
Uptake Confirmed no
Label Confidence high
In Vitro Functional Effect yes
Endosomal Escape Evidence
Peptide Concentration 0.5–10 µM CPP-AMO (typical 1–5 µM)
Rna Concentration Same as CPP-AMO (covalent conjugate)
Mixing Ratio Covalent CPP–AMO conjugate (1:1 peptide:AMO)
Formulation Format CPP-conjugated AMO (AVI Biopharma peptide–morpholino conjugate)
Formulation Components (RXRRBR)2XB peptide covalently conjugated to AMO
Size Nm
Zeta Mv
Model Scope in_vitro
Model Type in vitro
Cell Lines Or Primary Cells A-T lymphoblastoid cell line (AT203LA; heterozygous IVS28-159A>G)
Animal Model
Administration Route
Output Type splice correction + protein/kinase restoration
Output Value Strong splice correction and ATM protein restoration (~50% of WT by ELISA at effective doses); ATM kinase activity restored; radiosensitivity corrected.
Output Units
Output Notes CPP-AMO effective at ≥0.5–2.5 µM; demonstrates gene-dose effect (heterozygous vs homozygous).
Toxicity Notes Not explicitly quantified.
Curation Notes