Back to browse

EXP002295

Paper

Systemic peptide-mediated oligonucleotide therapy improves long-term survival in spinal muscular atrophy (2016)

Peptide

Pip6a

Sequence: Ac-(RXRRBRRXRYQFLIRXRBRXRB)-COOH

RNA

PMO (splice-switching antisense oligonucleotide)

All experiment fields

Experiment Id EXP002295
Paper Systemic peptide-mediated oligonucleotide therapy improves long-term survival in spinal muscular atr
Peptide Pip6a
Delivery Success Class no
In Vivo Flag no
Uptake Confirmed yes
Label Confidence high
In Vitro Functional Effect yes
Endosomal Escape Evidence
Peptide Concentration 25–500 nM
Rna Concentration 25–500 nM
Mixing Ratio 1:1 covalent conjugate
Formulation Format peptide–PMO conjugate
Formulation Components Pip6a–PMO
Size Nm
Zeta Mv
Model Scope in_vitro
Model Type in vitro
Cell Lines Or Primary Cells SH-SY5Y human neuroblastoma cells
Animal Model
Administration Route cell incubation
Output Type splice correction
Output Value ↑ full-length SMN2 transcript
Output Units
Output Notes Dose-dependent increase in FLSMN2; naked PMO inactive
Toxicity Notes no toxicity reported
Curation Notes